atrial septal defect (asd) is a common congenital anomaly that has low surgical mortality and morbidity. we report a very rare case of a low-lying asd, combined with the drainage of the inferior vena cava and the left superior vena cava into the left atrium. this combination was associated with an unroofed coronary sinus. we also describe an iatrogenic surgical diversion of the inferior vena ca...

Congenital   aortocaval   fistula in association with complex congenital heart disease has never been described before. We represent an adult with tetralogy of fallot and an undiagnosed subclavian artery to superior vena cava fistula in previous catheterisms. He underwent surgical correction, successfully. After 8 months post operation he was doing well with improved functional capacity and no ...

Congenital agenesis of the inferior vena cava is an uncommon congenital anomaly which can be misdiagnosed. Agenesis of the inferior vena cava has an incidence of 0.0005% to 1% in the general population [1]. The most common cause of agenesis of the inferior vena cava is the failure of embryological development between the sixth and the tenth weeks of gestation. Heterotaxy syndrome is associated ...

Congenital vascular anomalies are although rare but may cause serious complications. Vascular pathologies are best demonstrated by contrast enhanced computed tomography, with the advent of multidetector computed tomography and applying multiplanar reformation techniques. However, ultrasound color Doppler and catheter angiography are accessory imaging modalities utilized to rule out vascular ano...

Congenital abnormalities were present in 12 out of 30 (40%) children with extrahepatic portal hypertension of unknown cause, but in only 2 out of 17 (12%) children with extnahepatic portal hypertension secondary to umbilical vein catheterization or omphalitis. The most frequent abnormalities in this series and in published reports were atrial septal defect, malformation of the biliary tract, an...

congenital   aortocaval   fistula in association with complex congenital heart disease has never been described before. we represent an adult with tetralogy of fallot and an undiagnosed subclavian artery to superior vena cava fistula in previous catheterisms. he underwent surgical correction, successfully. after 8 months post operation he was doing well with improved functional capacity and no ...

A patient aged 25 years with lower extremity deep vein thrombosis in the course of vena cava inferior agenesis is described. This very rare malformation can be connected with chronic venous insufficiency or thrombotic complications. In such cases other congenital abnormalities should be excluded and suspicion of vena cava inferior agenesis should always be taken into consideration in young pati...

PATIENT Female, 50 FINAL DIAGNOSIS: Double superior vena cava Symptoms: - MEDICATION - Clinical Procedure: - Specialty: Nephrology. OBJECTIVE Anatomical anomaly/variation. BACKGROUND Superior vena cava anomalies are caused by variations in the development of the embryonic thoracic venous system. Duplication of the superior vena cava is a rare anomaly with an incidence in the general popul...

Scimitar syndrome or Felsons veno-lobar is a very rare congenital disease characterized by combination of cardiopulmonary abnormalities, including partial right-sided pulmonary venous drainage to the inferior vena cava, cavo-atrial junction, low on right atrium. We report case 53-year-old female patient who presented with recent gradually worsening dyspnea. The diagnosis was suspected chest x-r...

We report an interesting case of a man with a persistent left superior vena cava (PLSVC) with left azygos vein who underwent electrophysiological evaluation. Further evaluation revealed congenital dilated azygos vein, while a segment connecting the inferior vena cava (IVC) to the hepatic vein and right atrium was missing. The azygos vein drained into the superior vena cava, and the hepatic vein...