A successful anesthetic approach in a patient with Schwartz–Jampel syndrome
نویسندگان
چکیده
منابع مشابه
Anesthetic Approach for a Patient with Jeune Syndrome
Jeune syndrome (JS) is an autosomal recessive disease also known as asphyxiating thoracic dystrophy. A narrow bell-shaped thoracic wall and short extremities are the most typical features of the syndrome. Prognosis in JS depends on the severity of the pulmonary hypoplasia caused by the chest wall deformity. Most patient deaths are due to respiratory problems at early ages. Herein, we report a c...
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ژورنال
عنوان ژورنال: Saudi Journal of Anaesthesia
سال: 2018
ISSN: 1658-354X
DOI: 10.4103/sja.sja_393_17