Budd-Chiari Syndrome in a Patient with JAK2V617F and Factor V G1691A Mutations
نویسندگان
چکیده
منابع مشابه
Factor V G1691A (Leiden) is a major etiological factor in Egyptian Budd-Chiari syndrome patients.
OBJECTIVE Budd-Chiari syndrome is a multifactorial disease in which several prothrombotic disorders may predispose patients to the development of thrombosis at this uncommon location (hepatic veins). The aim of this study was to determine the prevalence and characteristics of inherited thrombophilia in Egyptian Budd-Chiari syndrome patients. METHODS The study included 47 Budd-Chiari syndrome ...
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Budd-Chiari syndrome (BCS) is a rare condition which occurs when there is obstruction of the hepatic veins. It includes any condition in which there is obstruction to venous flow from the small hepatic veins to the inferior vena cava. It should be differentiated from veno-occlusive disease in which the sinusoidal epithelial cells of the hepatic venules are damaged; this mainly occurs after stem...
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ژورنال
عنوان ژورنال: The West Indian Medical Journal
سال: 2014
ISSN: 0043-3144
DOI: 10.7727/wimj.2013.228