Common variable immunodeficiency disorder - An uncommon cause for bronchiectasis
نویسندگان
چکیده
منابع مشابه
Bronchiectasis caused by common variable immunodeficiency
Primary immunodeficiencies (PIDs) are characterized by impairment of one or more arms of the immune response, resulting in decreased defense, an increased number of infections, and, in certain cases, a higher incidence of autoimmune diseases and cancers.(1) Although PIDs are considered rare diseases, many of them are more common than are those currently diagnosed with the “heel prick” test. The...
متن کاملDisseminated bronchiectasis in an adult with common variable immunodeficiency
Primary immunodeficiencies (PID) are traditionally considered childhood diseases; however, adults account for 35% of all patients with PID. Antibody deficiencies, especially Common Variable Immunodeficiency (CVID), which have their peak incidence in adulthood, require a high suspicion index. Even though the estimated frequency of CVID is not high (1:25,000), high rates of under diagnosis and un...
متن کاملThrombocytopenic purpura associated with common variable immunodeficiency and bronchiectasis
Case report Boy with 13 years old diagnosed with thrombocytopenic purpura and a normal myelogram. He presented low levels of immunoglobulins (A = 7 mg / dl, M = 14,2mg / dl and G = 140 mg / dl). Immunophenotyping of lymphocytes was altered with CD19 = 7.9% (81cells / mm3); CD4 = 56.5% (574cells / mm3) and CD8 = 12.3% (125cells / mm3). The research of vaccine antibodies (tetanus, mumps) was nega...
متن کاملSevere bronchiectasis in a patient with common variable immunodeficiency.
BACKGROUND Bronchiectasis are common in Common Variable Immunodeficiency. These patients are prone to infection, leading to progressive lung destruction and accelerated FEV1 decline. CLINICAL CASE 40 year-old man, with recurrent respiratory infections, autoimmunity and diarrhea since age 7. At 17 CVID was diagnosed and IVIgG was started. During the following years, respiratory symptoms progre...
متن کاملCommon variable immunodeficiency - an update
Common variable immunodeficiency (CVID) describes a heterogeneous subset of hypogammaglobulinemias of unknown etiology. Typically, patients present with recurrent bacterial infections of the respiratory and gastrointestinal tract. A significant proportion of CVID patients develops additional autoimmune, inflammatory or lymphoproliferative complications. CVID is the most frequent symptomatic pri...
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ژورنال
عنوان ژورنال: Lung India
سال: 2014
ISSN: 0970-2113
DOI: 10.4103/0970-2113.142138