Diffuse Pulmonary Lymphangiomatosis
نویسندگان
چکیده
منابع مشابه
Diffuse pulmonary lymphangiomatosis: imaging findings.
Diffuse pulmonary lymphangiomatosis is a rare pulmonary disorder affecting the lymphatic channels from the mediastinum to the pleura. The disease usually occurs in children and young adults and frequently ends with death due to progressive course. Imaging findings of the disease are based on lymphatic involvement which appear as mediastinal soft tissue infiltration and thickening of pulmonary p...
متن کاملDiffuse pulmonary lymphangiomatosis with mediastinal affectation.
1. Morcel K, Camborieux L. Programmede recherches sur les aplasiesmüllériennes (PRAM)andGuerrierD.Mayer–Rokitansky–Küster–Hauser syndrome.Orphanet J Rare Dis. 2007;2:13. 2. Strübbe EH, Cremers CW, Wilemsen WN, Rolland R, Thijn CJ. The Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome without and with associated features: two separate entities? Clin Dysmorphol. 1994;3:192–9. 3. Vasquez JC, De la Ro...
متن کاملPathology analysis of a rare case of diffuse pulmonary lymphangiomatosis.
Diffuse pulmonary lymphangiomatosis (DPL) is a rare lymphatic disorder characterized by uncontrolled proliferation of lymphatic vessels. Histologically benign, however, it can lead to death because of its progression. In this paper, we would like to present an unusual case of diffuse pulmonary lymphangiomatosis involving a 28-year-old young female who was suffered chest pain and polypnea for on...
متن کاملA case of diffuse pulmonary lymphangiomatosis with unilateral lung invasion
Diffuse pulmonary lymphangiomatosis (DPL) is a rare interstitial lung disease characterized by intrathoracic lymphatic system abnormalities often with involvement of both lungs. Here, we report a 24-year-old male patient with DPL initially located in one lung, presenting only with transient fever. Resection of the right middle and lower lobes was performed for diagnosis and complete removal of ...
متن کاملSpleen, Non-Systemic Diffuse Lymphangiomatosis
Lymphangiomatosisis a rare disorder believed to be result from a developmental malformation of lymphatic system. Lymphangiomatosis involves bone, soft tissues, and viscera in a diffuse fashion. We describe an unusual case of splenic lymphangiomatosis in 41 years old female.
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ژورنال
عنوان ژورنال: Canadian Respiratory Journal
سال: 2013
ISSN: 1198-2241
DOI: 10.1155/2013/971350