Eosinophilic Granulomatosis with Polyangiitis: Diagnostic Dilemmas
نویسندگان
چکیده
منابع مشابه
Diaphragmatic paralysis in eosinophilic granulomatosis with polyangiitis.
La granulomatosis eosinofílica con poliangitis es una enfermead autoinmune que afecta a los pequeños vasos, su causa es esconocida y el retraso en su diagnóstico determina un peor ronóstico. Los pacientes pueden presentarse con algún grado de nsuficiencia respiratoria debida a asma, neumonía, hemorragia lveolar, tromboembolismo, así como problemas cardiovasculares neuromusculares1. Solo ocasion...
متن کاملEosinophilic Granulomatosis with Polyangiitis: An Overview
Eosinophilic granulomatosis with polyangiitis (EGPA) is a multisystemic disorder, belonging to the small vessel anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis, defined as an eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels, associated with asthma a...
متن کاملKey words: employment, work disability, quality of life, granulomatosis with polyangiitis, eosinophilic granulomatosis with polyangiitis, microscopic polyangiitis
Clinical and Experimental Rheumatology 2017 1Department of Internal Medicine, National Referral Centre for Rare Autoimmune and Systemic Diseases, Cochin Hospital, Assistance PubliqueHôpitaux de Paris (AP-HP), Université Paris Descartes, Paris; 2Department of Occupational and Environmental Diseases, Cochin Hospital, AP-HP, Université Paris Descartes, Paris, France. Lucas Benarous, MD* Benjamin T...
متن کاملEosinophilic Granulomatosis with Polyangiitis Manifested by Cholecystitis and Mononeuritis Multiplex: A Case Report
Eosinophilic granulomatosis with polyangiitis formerly named “Churg-Strauss syndrome (CSS)” is a systemic disease with bronchial asthma, hypereosinophilia, and systemic vasculitis. We report a case of CSS with cholecystitis and mononeuritis multiplex. A 50-year-old woman with a history of sinusitis and bronchial asthma of 8 years’ duration was referred with a complaint of left-hand deformity an...
متن کاملOtologic and Rhinologic Manifestations of Eosinophilic Granulomatosis with Polyangiitis.
BACKGROUND Eosinophilic granulomatosis with polyangiitis (EGPA) is a systemic autoimmune disease that manifests as asthma, recurrent sinusitis and peripheral eosinophilia. In this study, we investigated the clinical features of the ear and nasal manifestations of EGPA in comparison with those of granulomatosis with polyangiitis (GPA). MATERIALS AND METHODS Twenty-one patients diagnosed with E...
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ژورنال
عنوان ژورنال: Internal Medicine
سال: 2018
ISSN: 1220-5818
DOI: 10.2478/inmed-2018-0007