Hereditary Multiple Exostoses (HME) with Peroneal Nerve Compresion: A Case Report
نویسندگان
چکیده
Introduction: Hereditary multiple exostosis (HME) is a hereditary disorder characterized by osteochondromas. Clinical symptoms can result from compression of adjacent structures such as peripheral nerves. In Indonesia, HME with nerve cases have rarely reported. Presentation Case: An eleven-year-old female complaining left knee joint pain and progressive masses in lower leg since 6 years ago. This complains followed numbness difficulty to dorso flexion motion on ankle four months Physical examination showed the bony was detected at lateral upper third measuring about six into eight centimeters. Range patient had difficult flexion. X-ray imaging viewed demonstrates appearance involving distal femoral, proximal fibula, tibia fibula bone. MR Imaging revealed cartilage cap head thin less 1.5 cm axially specimen peroneal compression. The underwent wide resection. Intraoperative findings decompression. Medical rehabilitation for physiotherapy advised. results follow-up after 2 years, no feels able additional bumps other areas body. These lesions may arise any bone which pre-formed cartilage. Nerve syndromes are neurological complex symptom caused mechanical or dynamic specific single segment. MRI excellent demonstration blood vessels compromise represents choices nerves thickness criterion osteochondromas differentiation exostotic grade. Complete resection importance cartilaginous prevent recurrence. decompressing that pressured vascular problems occured. Conclusion: an inherited It important monitor all especially if growth osteochondroma. surgical excision, complete tumor, preventing
منابع مشابه
Acetabular dysplasia associated with hereditary multiple exostoses. A case report.
Hereditary multiple exostoses is an autosomal dominant disorder characterised by multiple osteochondromata, most commonly affecting the forearm, knee and ankle. Osteochondromata of the proximal femur have been reported to occur in 30% to 90% of affected patients with coxa valga in 25%. Acetabular dysplasia is rare but has been described. This is the first report of a patient requiring surgical ...
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Hereditary multiple exostoses (HME) is a skeletal disorder which primarily affects enchondral bone during growth. It is characterised by multiple exostoses, usually arising in the juxtaepiphyseal region of the long bones. Exostoses that affect "almost every bone in the body" were first mentioned by John Hunter in his Lectures on the principles of surgery in 1786.1 The first family affected by H...
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ژورنال
عنوان ژورنال: International Journal of Medical Physics, Clinical Engineering and Radiation Oncology
سال: 2023
ISSN: ['2168-5436', '2168-5444']
DOI: https://doi.org/10.4236/ijmpcero.2023.122006