Management of supravalvar aortic stenosis and severely depressed left ventricular function in a neonate with Williams syndrome
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چکیده
منابع مشابه
Transapical transcatheter aortic valve implantation in a heart transplant recipient with severely depressed left ventricular function.
Transcatheter aortic valve implantation (TAVI) is becoming a valuable alternative to surgical aortic valve replacement in non-operable and high-risk surgical patients. As the population of heart donors and recipients ages, the prevalence of degenerative valvular disease after transplantation will increase. The optimal treatment strategy of valvulopathies in these patients with extensive comorbi...
متن کاملImproved surgical outcome for chronic severe aortic regurgitation with severely depressed left ventricular systolic function.
hronic severe aortic regurgitation (AR) imposes a comined pressure and volume overload on the left ventricle LV). Fortunately, preload reserve and compensatory hyperrophy allow most patients with chronic severe AR to aintain normal LV systolic function for many years. Most uch patients are asymptomatic and have an excellent rognosis (1–3). Over the course of time, adverse loading onditions may ...
متن کاملSUPRAVALVAR AORTIC STENOSIS IN CHILDREN REPORT OF THIRTEEN CASES
During 15 years from 1975 to 1990, thirteen cases of supravalvar aortic stenosis were admitted at the pediatrics department of Shahid Rajai Heart Hospital, Tehran. All patients were subjected to cardiac catheterization and a angiocardiography. Patients ranged in age from 3.5 years to 14 years with a mean of 8.7 years. Seventy seven percent of childen were male. Eight cases (61.5%) had Wil...
متن کاملSupravalvar aortic stenosis.
one manifestation of the idiopathic hypercalcaemia of infancy syndrome, and the possible aetiologies are discussed. Another presentation of supravalvar aortic stenosis is in the so-called familialform, but there may exist considerable confusion between these two forms, as less than 50 per cent of those without physical stigmata have a positive family history, and the severeform of the idiopathi...
متن کاملLeft ventricular outflow obstruction: subaortic stenosis, bicuspid aortic valve, supravalvar aortic stenosis, and coarctation of the aorta.
Left ventricular outflow tract obstructions (LVOTOs) encompass a series of stenotic lesions starting in the anatomic left ventricular outflow tract (LVOT) and stretching to the descending portion of the aortic arch (Figure 1). Obstruction may be subvalvar, valvar, or supravalvar. These obstructions to forward flow may present alone or in concert, as in the frequent association of a bicuspid aor...
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ژورنال
عنوان ژورنال: European Journal of Cardio-Thoracic Surgery
سال: 2009
ISSN: 1010-7940
DOI: 10.1016/j.ejcts.2009.01.020