Two Separated Ileal Adenocarcinomas in Neurofibromatosis Type 1

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Two Separated Ileal Adenocarcinomas in Neurofibromatosis Type 1

Patients with neurofibromatosis-1 (NF-1) have increased susceptibility to a variety of malignancies. Here, we document a rare case of two separated ileal adenocarcinomas in NF-1. The adenocarcinomas were surrounded by a diffuse tubular adenomatous lesion of the mucosa, and ganglion cells were scattered in the NF background. We found this case meaningful for several reasons: two separated adenoc...

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ژورنال

عنوان ژورنال: Yonsei Medical Journal

سال: 2007

ISSN: 0513-5796

DOI: 10.3349/ymj.2007.48.6.1039