Familial amyloid polyneuropathy: hypertrophy of ligaments supporting the spinal cord.
نویسندگان
چکیده
We describe characteristic spinal MR findings of two cases of familial amyloid polyneuropathy (FAP). Both cases showed leptomeningeal enhancement on contrast-enhanced T1-weighted image. In addition, three-dimensional constructive interference in steady-state imaging demonstrated thickening of the ligaments, other connective tissues within the spinal canal, dura matter, and dorsal nerve roots. These findings in FAP are felt to represent amyloid deposition.
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عنوان ژورنال:
- AJNR. American journal of neuroradiology
دوره 25 9 شماره
صفحات -
تاریخ انتشار 2004