A familial case of scleroderma en coup de sabre.

نویسندگان

  • A Patrizi
  • S Marzaduri
  • R Marini
چکیده

Sir, Linear scleroderma represents a rare disease, more often observed in the pediatric age group. The lower extremities are usually involved; less commonly it affects the frontoparietal area and the anterior scalp. Recently, a large case series of frontoparietal scleroderma en coup de sabre has been reported (1), but in this series, as well as in the English language literature, to the best of our knowledge, no familial cases have ever been reported. We report herein 2 patients, a 14-year-old girl and her grandfather, affected by frontoparietal scleroderma. Both patients present an atrophic lesion on the midline of the forehead extending from the scalp to the medial side of the eyelids, which is the seat of frontoparietal scleroderma most often reported in the literature (2).

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عنوان ژورنال:
  • Acta dermato-venereologica

دوره 80 3  شماره 

صفحات  -

تاریخ انتشار 2000