Thoracic Duct Decompression for Protein-Losing Enteropathy in Failing Fontan Circulation.
نویسندگان
چکیده
An infrequent but devastating late complication of Fontan circulation is protein-losing enteropathy (PLE), which results from unbalanced lymphatic homeostasis. Surgical decompression of the thoracic duct by redirecting its drainage to the pulmonary venous atrium has been introduced recently as a possible treatment. This report describes a single-institution experience with this innovative procedure in 2 patients with failing Fontan circulation with PLE refractory to optimized medical therapy.
منابع مشابه
Heart transplantation in single-ventricle physiology with failed fontan circulation
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Patients were observed after the Fontan operation to determine the frequency and severity of protein-losing enteropathy. A total of 427 patients who survived for 30 days after the Fontan operation, performed between 1973 and January 1987, were analyzed and, thus far, protein-losing enteropathy has developed in 47 of 427. The cumulative risk for the development of protein-losing enteropathy by 1...
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Reference 1. Lenz D, Hambsch J, Schneider P, Häusler HJ, Sauer U, Hess J, Tárnok A: Protein-losing enteropathy in patients with Fontan circulation: is it triggered by infection? Crit Care 2003 7:185190. Correction Correction: Protein-losing enteropathy in patients with Fontan circulation: is it triggered by infection? Dominik Lenz1, Jörg Hambsch2, Peter Schneider3, Hans-Jürgen Häusler2, Ursula ...
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1 Hill D, Feldt R, Porter C, Puga F, Danielson G, Perrault J. Protein-losing enteropathy after Fontan operation: a preliminary report. Circulation 1989;80(suppl II):490. 2 Rothman A, Snyder J. Protein-losing enteropathy following the Fontan operation: resolution with prednisone therapy. Am HeartJ 1991;121:618-619. 3 Rychick J, Piccoli DA, Barber G. Usefulness of corticosteroid therapy for prote...
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عنوان ژورنال:
- The Annals of thoracic surgery
دوره 101 6 شماره
صفحات -
تاریخ انتشار 2016