Plexiform neurofibroma in a 16-year-old girl
نویسندگان
چکیده
Plexiform neurofibroma is a rare, poorly defined benign tumor of the peripheral nerve sheath. It spreads out just under the skin, or deeper in the body, and occurs exclusively in patients with neurofibromatosis type I. Facial plexiform neurofibroma may produce various degrees of cosmetic and functional deformities in the head and neck region. It is a virtually pathognomonic and often disabling feature of neurofibromatosis type I. We present a case of plexiform neurofibroma in an 18-year-old female.
منابع مشابه
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عنوان ژورنال:
دوره 7 شماره
صفحات -
تاریخ انتشار 2012