Arrhythmogenic right ventricular cardiomyopathy in monozygotic twin sisters, and persistent left superior vena cava in one complicating implantation of ICD.

Persistent left superior vena cava. Use of an innominate vein between left and right superior caval veins for the placement of a right ventricular lead during ICD/CRT implantation.

CRT-D Implantation Through a Persistent Left Superior Vena Cava

A persistent left superior vena cava (PLSVC) was present in a 74 year-old man with dilated cardiomyopathy undergoing implantation of a cardiac resynchronization therapy device with defibrillator (CRT-D). A dual-coil active-fixation defibrillator lead was positioned in the right ventricular apex, followed by a SonR active fixation lead in the right atrial free wall. The coronary sinus lead was a...

Substernal ICD lead implantation in a patient not suitable for subcutaneous ICD implantation without venous access due to superior vena cava syndrome

Case report A 51-year-old man with a dilated cardiomyopathy with a left ventricular ejection fraction of 10% was transferred to our hospital. The patient was known to have superior vena cava (SVC) syndrome related to a JAK2 mutation. He had several hospital admissions in the past with heart failure. His current NYHA class is II–III on optimal heart failure medication. During his hospital stay h...

Persistent Left Superior Vena Cava in Patients Undergoing Cardiac Device Implantation: Clinical and Long-Term Data

BACKGROUND Persistent left superior vena cava (LSVC) is a rare congenital venous anomaly that may be found at the time of cardiac device lead insertion. METHODS In this case series, we present clinical and long-term data of five patients with LSVC who underwent pacemaker (PM) or cardioverter defibrillator (ICD) implantation during the period of 10 years. RESULTS Left-sided venous approach w...

Successful dual chamber ICD implantation via a persistent left superior vena cava after ratchet syndrome

Device implantations may be challenging in patients with venous abnormalities. The most common congenital variation, frequently associated with other congenital abnormalities, is a persistent left superior vena cava (PLSVC), and successful atrial and ventricular lead implantation via a PLSVC have both been reported [1]. “Ratchet syndrome” has also been reported as a rare complication after a ne...