A case of severe pulmonary hypertension associated with common arterial trunk and VSD in a 9 years old child

Authors

Abstract:

Background: Common arterial trunk (CAT) is a rare congenital heart disease, and often leads to the early development of pulmonary hypertension and disability. Among the critical structural heart defects, the frequency of CAT is 3%, which reflects the severe hemodynamic disturbances. The natural course of the disease is characterized by a high mortality rate up to 88% during the first year of life. We introduce a patient with common arterial trunk disease. Case presentation: The article describes a case of a 9-year old boy with a diagnosis of type I common arterial trunk (CAT) that rejected recommendations of many physicians for many years. At 7 months, the baby was diagnosed as CHD and at 3 years, a cardiac catheterization was performed and the final diagnosis was common arterial trunk, type I with defect of interventricular septum and pulmonary hypertension. During, parents refused the operation. The health status of the last examination was bad due to high pulmonary hypertension and chronic arterial hypoxemia. Drug therapy continued with bosentan, sildenafil, captopril, kudesang, spironolactone and aspirin Conclusion: The late detection of children with CAT or late surgery leads to the rapid progression of pulmonary hypertension and significantly reduces the patientchr('39')s chances for performing surgical correction of the defect.

Upgrade to premium to download articles

Sign up to access the full text

Already have an account?login

similar resources

Uncommon Manifestation of Complex Partial Seizure in a 7 Years old Child ; a Case Report

Complex partial seizures are known as focal seizures with impaired awareness. Excluding the first year of life, complex partial seizures are the most frequent type of seizures in patients with epilepsy. A detailed history of the patient and family members is a vital element in diagnosing seizures. Although rare, psychotic and anxiety symptoms in individuals may be the result of the seizure. A 7...

full text

a comparison of linguistic and pragmatic knowledge: a case of iranian learners of english

در این تحقیق دانش زبانشناسی و کاربردشناسی زبان آموزان ایرانی در سطح بالای متوسط مقایسه شد. 50 دانش آموز با سابقه آموزشی مشابه از شش آموزشگاه زبان مختلف در دو آزمون دانش زبانشناسی و آزمون دانش گفتار شناسی زبان انگلیسی شرکت کردند که سوالات هر دو تست توسط محقق تهیه شده بود. همچنین در این تحقیق کارایی کتابهای آموزشی زبان در فراهم آوردن درون داد کافی برای زبان آموزان ایرانی به عنوان هدف جانبی تحقیق ...

15 صفحه اول

Adrenocortical carcinoma in a 8 years old child: a Case Report

Background:Unilateral tumors or masses of the adrenal gland are common. They are categorized as either functional (hormone-secreting) or silent and as either benign or malignant. Adrenocortical tumors are rare in childhood, with an incidence of 0.3-0.5 cases per one million child-years. Almost half of childhood tumors are adrenocortical carcinomas (ACC). Most ACCs are sporadic, but specialy i...

full text

Common arterial trunk associated with a homeodomain mutation of NKX2.6.

Persistent truncus arteriosus (PTA) is a failure of septation of the cardiac outflow tract (OFT) into the pulmonary artery and the aorta. A common arterial trunk (CAT) is often diagnosed as PTA in the absence of evidence of embryological mechanism. We have used autozygosity mapping of a large consanguineous family segregating CAT to map the causative locus to chromosome 8p21. An F151L mutation ...

full text

Drug-induced interstitial nephritis in a 9-year-old child: A case report

Drug-induced acute interstitial nephritis (DI-AIN) is a common cause of AKI and leading to CKD and ESRD Although any drug can potentially cause DI-AIN, antibiotics, non-steroidal anti-inflammatory drugs and proton pump inhibitors are the most common culprits. In the present study, we report a 9-year-old child with drug-induced interstitial nephritis (cefotaxime, vancomycin, and acyclovir). it s...

full text

Hypophosphatemia Dependent Rickets with Failure to Thrive (FTT) in a 4- Years Old Child: a Case Report

BackgroundRickets is a disorder due to impaired metabolism of bone mineralization which caused by low concentrations of extra-cellular calcium or phosphate. In children, hypophosphatemic rickets (HR) happen malabsorption of phosphate and increasing of renal tubular loss.Case Presentation We present the case of a 4-year-old girl who had medical history of HR with failure to thrive (FTT). Child h...

full text

My Resources

Save resource for easier access later

Save to my library Already added to my library

{@ msg_add @}


Journal title

volume 11  issue None

pages  454- 457

publication date 2020-06

By following a journal you will be notified via email when a new issue of this journal is published.

Keywords

Hosted on Doprax cloud platform doprax.com

copyright © 2015-2023