A Case Study of Hypomelanosis of Ito

Among nevoid causes of hypopigmentations; incontinentia pigmenti achromians (Hypomelanosis of Ito) is a neurocutaneous syndromes characterized by distinctive macular, linear or irregular whorls or swirls of Hypopigmentations. Unrelated to incontinentia pigmenti, the loss of pigment begins spon­taneously during infancy or early childhood and is of Particular importance because of the falt that many patients have associated Internal anomalies and manifestations, (seizure disorders, delayed deve­lopment, musculoskeletal anomalies or occular disturbances). A case of Hypomelanosis of Ito with generalized seizure was presented in a 7 month-old male; this will definitively discloses anthre rare cause of convulsion to look fore in pediatric practice.