marfan’s syndrome (mfs) is a genetic disorder associated with autosomal dominant inheritance. in mfs, the most prevalent cause of death is cardiovascular involvement. here we introduce a family with a severe penetration of mfs. eleven members of this family have mfs (father, two daughters, three sons, and five grandchildren). the most common cardiac involvement in our patients was mitral valve ...

Education and support based on family’s needs may reduce anxiety and increase satisfaction of family members of hospitalized patients in Intensive Care Unit (ICU). This study was conducted to determine the effect of educational-supportive intervention on satisfaction of family members. In this quasi-experimental study, 154 participants of family members of hospitalized patients in ICU in ...

background: there are many risk factors besides age and immune suppression for herpes zoster. family history as a risk factor is suggested in some recent studies. the aim of this study was to evaluate the association between herpes zoster and family history. methods: this case-control study was undertaken in farshchian hospital, hamadan, iran. “case group” included patients with confirmed diagn...

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Background: Alopecia Areata (AA) is a recurrent non-scarring type of hair loss that can affect any hair-bearing area. Prognosis of AA is unpredictable and most patients experience more than one episode of hair loss. The purpose of this study was to investigate the relationship between the severity of AA with respect to age of onset, nail involvement, family history, number of recurrences and du...

how to cite this article: karimzadeh p, jafari n, nejad biglari hb, jabbehdari s, alizadeh m, alizadeh gh, nejad biglari hm, sanii s. the clinical features and diagnosis of adrenoleukodystrophy: a case series of iranian family. iran j child neurol. winter 2016; 10(1):61-64. abstract objective adrenoleukodystrophy disorder is one of the x-linked genetic disorders caused by the myelin sheath brea...

background: this study was designed to determine the frequency of microsatellite instability (msi) in young iranian pa­tients with endometrial carcinoma and to evaluate its association with histopathologic and clinical features of disease. methods : microsatellite status was analyzed in 23 patients with endometrioid type endometrial cancer who were less than 55 years. clinicopathologic characte...

The main concern with respect to discharge of patients from hospital after 131-I therapy is contamination of their surroundings and exposure of people who are in close contact with them. In this study, we evaluated absorbed dose received by homemates of these patients within one week of discharge from hospital. This study was based on 100 patients (23 patients with thyroid cancer together...

introduction schizophrenia is a severe mental illness that causes lack of insight into the disease and the drugs will experience episodes of relapses. in addition, it is a progressive disorder effect on the individual and involved their family. this study aimed to determine the effects of family-centered empowerment model on the attitude and medication compliance of patients with schizophrenia....