نتایج جستجو برای: dhplc

تعداد نتایج: 390  

Journal: :Journal of medical genetics 2002
D J Halliday S Hutchinson L Lonie J A Hurst H Firth P A Handford P Wordsworth

Marfan syndrome (MFS) is one of the major heritable disorders of connective tissue with a prevalence of between 1 in 5-10 000. 2 It is characterised by features in the cardiovascular, ocular, and musculoskeletal systems and the Ghent criteria form a useful framework for its diagnosis. Mutations in FBN1 encoding the extracellular matrix protein fibrillin-1 classically cause MFS. Fibrillin-1, com...

Journal: :Journal of medical genetics 2003
J Mogensen A Bahl T Kubo N Elanko R Taylor W J McKenna

The recent achievement of the human genome project has led to the identification of many disease genes in common hereditary conditions, in which patients and their relatives would benefit from genetic diagnosis. This has increased the need for simple, sensitive, and cost effective methods of mutation analysis. However, the “gold standard” of mutation analysis, direct sequencing, is still an exp...

2010
Mark Braschinsky Riin Tamm Christian Beetz Elena Sachez-Ferrero Elve Raukas Siiri-Merike Lüüs Katrin Gross-Paju Catherine Boillot Federico Canzian Andres Metspalu Sulev Haldre

BACKGROUND Hereditary spastic paraplegia (HSP) is a clinically and genetically heterogeneous disorder that can be an autosomal-dominant, autosomal-recessive, or X-linked disease. The most common autosomal-dominant form of the disease derives from mutations in the SPAST gene. METHODS The aim of this study was to analyze 49 patients diagnosed with HSP from the Estonian population for sequence v...

Journal: :Clinical chemistry 2004
Carol M Preissner William M Reilly Richard C Cyr Dennis J O'Kane Ravinder J Singh Stefan K G Grebe

DGGE and SSCA. Hum Mutat 1996;7:114–22. 6. Jorge SB, Melo MB, Costa FF, Sonati MF. Screening for mutations in human -globin genes by nonradioactive single-strand conformation polymorphism. Braz J Med Biol Res 2003;36:1471–4. 7. Foglietta E, Deidda G, Graziani B, Modiano G, Bianco I. Detection of -globin gene disorders by a simple PCR methodology [Erratum published in: Haematologica 1996;81:XVI]...

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