X linked hypohidrotic ectodermal dysplasia (XHED) affects many epithelial functions, including sweat gland formation. Female carriers who manifest XHED may have defective dentition or a patchy distribution of sweating or both, as determined by starch and iodine sweat testing. Such sweat testing can be useful in assigning carrier status to at risk females in XHED families, and in obtaining an ac...

Ectodermal dysplasia is a hereditary disorder that occurs due to consequence of disturbances in the ectoderm of the developing embryo. It is usually accompanied by lack of sweat glands and a partial or complete absence of primary and/or permanent dentition. A case report illustrating the prosthetic rehabilitation by flexible and removable partial denture for a girl child of 9 years with Ectoder...

Hay-Wells syndrome is a rare form of ectodermal dysplasia initially described by Hay and Wells in 1976. It is an autosomal dominant disorder with varying forms of expression featuring congenital abnormalities of the skin, hair, teeth, nails and sweat glands. The present report describes the case of a 17-yearold white boy, the son of nonconsanguineous parents, who presented ankyloblepharon filif...

Ectodermal dysplasia is a hereditary disorder characterized by involvement of abnormal nails, abnormal hair, abnormal or missing sweat glands and also abnormal dentition. The oral manifestation of the disease depends on the severity of the ectoderm involved. The Prosthodontic management of such patients with dysplastic condition necessitates a multidisciplinary approach. However the definitive ...