in this case report we will describe a rare association between anhyrotic ectodermal dysplasia (aed) and immunodeficiency and autoimmunity [in our case: idiopathic thrombocytopenic purpura (itp) and crohn disease]. aed is a rare congenital disorder characterized by sparse hair, abnormal teeth and anhidrosis due to lack of eccrine glands. the survey of 87 cases with (aed) revealed only one irrit...

ectodermal dysplasia is a hereditary disorder associated with abnormal development of embryonic ectodermally-derived organs including teeth, nails, hair and sweat glands. hypodontia of the primary and permanent dentition is the most common oral finding. therefore, affected patients need dental prosthetic treatments during their developmental years. this report presents two cases of children aff...

alveolar ridge is underdeveloped in ectodermal dysplasia (ed). the available treatment plans include fixed, removable or implant-supported prostheses, alone or in combination. a 5 year-old boy was referred for treatment to the department of prosthodontics, tehran university of medical sciences with the chief complaint of missing teeth. prosthodontic treatment was performed to improve masticatio...

Ectodermal Dysplasia is a hereditary disorder commonly associated with trichodysplasia (abnormal hair), onchodysplasia nails), dyshidrosis or missing sweat glands) and abnormal dentition. Due to ectodermal dysplasia, for missing, abnormally shaped, mal-positioned teeth, wide range of prosthetic options are available oral rehabilitation. This case report represents prosthodontic rehabilitation c...

Background: This study aimed to examine the effects of ectodermal dysplasia (ED) on transverse width maxillary bone.

Ectodermal dysplasia is a rare entity with incidence of 1 in 1,00,000 births male predominance. Most commonly it presents appendageal abnormality facial dysmorphism. The two most common types ectodermal dysplasias are hypohidrotic (Christ-Siemens-Touraine syndrome) and hidrotic (Clouston syndrome). Clinical recognition varies depending on severity symptoms associated complications. prognosis go...

the ellis-van creveld (evc) syndrome is a chondroectodermal dysplasia and is characterized by the cardinal features of disproportionate short stature, polydactyly, hidrotic ectodermal dysplasia, and congenital heart malformations, along with other skeletal and dental abnormalities. it is a rare condition, with very few cases reported in the medical literature. it is inherited as an autosomal re...

objectives: ectrodactyly-ectodermal dysplasia-clefting syndrome (eec) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. this study presents an iranian case with classic features and oral complications.   case: we report a 20-year old female with all manifestations of this syndrome. the simultaneous presence of these three malformations is extremely rar...

Ectodermal dysplasia, which affects ectodemal derivatives, currently is an X-linked recessive inheritary hypohydrotic ectodermal dysplasia. Patients with ectodermal dysplasia usually characterized by congenital teeth loss, abnormal teeth and inherited through female carriers. In this case report, we present a 5 years old boy of China ethnicity with mandibular anodontia, a rare dental dysplasia ...

Purpose: The study showed a patient with Ectodermal Dysplasia (ED) who was treated implants and fixed dental prosthesis by multidisciplinary team.