Congenital diaphragmatic hernia is a very serious congenital defect associated with high mortality rate. The syndrome is characterized by migration of abdominal viscera to thoracic cavity a variable degree of pulmonary hypoplasia associated with pulmonary hypertension caused by alteration of pulmonary vessels diameter increased muscularisation of pulmonary arteries and decreased compliance of t...

OBJECTIVE One and one half ventricle repair is a surgical option for congenital cardiac anomalies characterised by right ventricle (RV) hypoplasia and/or dysplasia. METHODS From March 1994 to March 2001, eight patients (mean age 9.1 years, range 7 months to 35 years) with hypoplastic and/or dysplastic RV underwent correction of their intracardiac anomaly in association with a BCPS (one and on...

purpose : to report a new familial presentation of hypoplasia and absence of superior rectus in the form of unilateral monocular elevation deficiency case report : a 7-year-old boy was referred to our center (poostchi eye clinic) with a chief complaint of ocular misalignment in his right eye since birth. one of his siblings was a known case of unilateral monocular elevation deficiency and was o...

When most of the centers in India do not entertain the patients with hypoplastic left heart syndrome, the original authors of the article in the present issue should be congratulated for the attempt of treating this patient with hybrid procedure. It’s a spectacular beginning. The development of staged reconstructive surgery for hypoplastic left heart syndrome (HLHS) by Norwood and colleagues in...

Becker's naevus is an acquired persistent asymmetrical area of skin pigmentation, sometimes showing evidence of increased androgen sensitivity, and colocalizing with other developmental anomalies. We report a 30-year-old woman with clinical findings compatible with Becker's naevus on her right breast accompanied with hypoplasia of ipsilateral breast.

Fi uax 1. Apical four-chamber views from preoperative two-dimensional echocardiogram showing dropout of interventriculan/septal echoes (left panel). Peripheral venous D5W injection (middle panel) at first opacifles only right atrium and ventricle, with no right-to-left shunt and possible left-to-right shunt as indicated by negative contrast effect in the right ventricle. With a premature beat, ...

introduction: nicotinamide adenine dinucleotide phosphate (nadph) oxidase-2 (nox2) is one of the predominant sources of ros production during myocardial ischemia-reperfusion and can be induced by angiotensin ii. the evidence suggests that pharmacological blockers of renin-angiotensin system can exert direct tissue effects independent of their ability to regulate blood pressure. the mechanism(s)...