Two patients with congenital mitral incompetence and coarctation of the aorta are presented. One patient had associated patent ductus arteriosus, bicuspid aortic valve, and endocardial fibroelastosis. The diagnosis in the two patients presented is well established by clinical, laboratory, and surgical findings and also by necropsy examination in one case. It is proposed that the rarity of repor...

Congenital mitral valve stenosis is a rare pathology. In this study, we aimed to present our surgical approach and successful valve repair to a case with congenital mitral valve stenosis combined with left persistent superior vena cava. Conservative surgery of the congenital mitral valve stenosis can be performed with acceptable early and midterm outcome in terms of mortality and reoperation ra...

When assessing the function of the mitral valve at operation by palpation or inspection, the surest way to prevent systemic (cerebral) embolism is to have the ascending aorta occluded by a clamp. A technique is described which allows safe assessment of mitral valve function by aortic root and left ventricular perfusion, giving a beating-heart preparation with the aorta cross-clamped. This metho...

Fifty-three specimens in which the primary diagnosis in life was coaretation of the aorta were examined; only nine had a mitral valve of normal size and configuration. Ten specimens had a normally formed valve mechanism which was small in comparison to both tricuspid valve and left ventricle. Three other specimens had a normally formed but small valve which exhibited a short free margin of the ...

Fifty-three specimens in which the primary diagnosis in life was coaretation of the aorta were examined; only nine had a mitral valve of normal size and configuration. Ten specimens had a normally formed valve mechanism which was small in comparison to both tricuspid valve and left ventricle. Three other specimens had a normally formed but small valve which exhibited a short free margin of the ...

The therapeutic implications of bicuspid aortic valve associations have come under scrutiny in the transcatheter aortic valve implantation era. We evaluate the spectrum of mitral valve disease in patients with bicuspid aortic valves to determine the need for closer echocardiographic scrutiny/follow-up of the mitral valve. A retrospective analysis of echocardiograms done at a referral hospital o...

The strategy for an infant with congenital mitral stenosis should be determined by three important factors: left ventricular volume, the degree of the systemic outflow tract obstruction, and the type of mitral valve dysfunction. A successful staged biventricular repair in early infancy for a patient who had congenital mitral stenosis with short chordae, hypoplastic left ventricle and coarctatio...

prolapsed mitral valve syndrome is a common, benign disorder with prevalence of %0.3-6 in population. this syndrome also is known as barlows syndrome and flaapy mitral valve syndrome. prolapsed mitral valve is the dropping of one or two mitral valve leaflet(s) into the left atrium during ventricular systole. this malformation leads to incomplete closing of mitral valve and regurgitates the bloo...

17. Shone JD, Sellers RD, Anderson RC, Adams P Jr, Lillihei CW, Edwards JE: The developmental complex of "parachute mitral valve," supravalvar ring of the left atrium, subaortic stenosis and coarctation of the aorta. Am J Cardiol 11: 714, 1963 18. Ellison RC, Restieaux NJ: Vectorcardiography in Congenital Heart Disease. Philadelphia, W.B. Saunders Co, 1972, p 196 19. Heath D, Edwards JE: The pa...