نتایج جستجو برای: dominant mutation

تعداد نتایج: 404478  

Journal: :Investigative ophthalmology & visual science 2014
Lori S Sullivan Daniel C Koboldt Sara J Bowne Steven Lang Susan H Blanton Elizabeth Cadena Cheryl E Avery Richard A Lewis Kaylie Webb-Jones Dianna H Wheaton David G Birch Razck Coussa Huanan Ren Irma Lopez Christina Chakarova Robert K Koenekoop Charles A Garcia Robert S Fulton Richard K Wilson George M Weinstock Stephen P Daiger

PURPOSE To identify the cause of retinitis pigmentosa (RP) in UTAD003, a large, six-generation Louisiana family with autosomal dominant retinitis pigmentosa (adRP). METHODS A series of strategies, including candidate gene screening, linkage exclusion, genome-wide linkage mapping, and whole-exome next-generation sequencing, was used to identify a mutation in a novel disease gene on chromosome ...

Journal: :American Journal of Physiology-Endocrinology and Metabolism 2006

Journal: :Investigative ophthalmology & visual science 2006
Yizhi Liu Xinyu Zhang Lixia Luo Mingxing Wu Ruiping Zeng Gang Cheng Bin Hu Bingfen Liu Jack J Liang Fu Shang

PURPOSE To identify the mutation and the underlying mechanism of cataractogenesis in a five-generation autosomal dominant congenital lamellar cataract family. METHODS Nineteen mutation hot spots associated with autosomal dominant congenital cataract have been screened by PCR-based DNA sequencing. Recombinant wild-type and mutant human alphaB-crystallin were expressed in Escherichia coli and p...

Journal: :The Journal of biological chemistry 1992
Y W Hwang M Carter D L Miller

A method has been developed to search for the elongation factor Tu (EF-Tu) domain(s) that interact with elongation factor Ts (EF-Ts). This method is based on the suppression of Escherichia coli EF-Tu-dominant negative mutation K136E, a mutation that exerts its effect by sequestering EF-Ts. We have identified nine single-amino acid- substituted suppression mutations in the region 146-199 of EF-T...

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