نتایج جستجو برای: dominant mutation

تعداد نتایج: 404478  

Journal: :iranian journal of public health 0
habib onsori dept. of genetics, marand branch, islamic azad university, marand, iran. mohammad rahmati dept. of clinical biochemistry, faculty of medicine, tabriz university of medical sciences, tabriz, iran. davood fazli dept. of biology, payame noor university (pnu), tehran, iran.

mutations in the gjb2 gene are the most common known cause of hereditary congenital hearing loss. rapid genomic dna extraction (rgde) method was used for genomic dna extraction. after amplification of coding region of cx26 gene with specific primers, expected pcr products with 724bp length were subjected to direct sequencing in both directions. we describe here a novel heterozygous -t to -c tra...

ژورنال: :gene, cell and tissue 0
farah talebi department of genetic, faculty of sciences, shahid chamran university of ahvaz, ahvaz, ir iran farideh ghanbari department of genetic, faculty of sciences, shahid chamran university of ahvaz, ahvaz, ir iran; department of genetic, faculty of sciences, shahid chamran university of ahvaz, ahvaz, ir iran. tel/fax: +98-6136233884 javad mohammadi asl department of medical genetics, faculty of medicine, ahvaz jundishapur university of medical sciences, ahvaz, ir iran

conclusions bioinformatics analyses using sift, mutation taster and polyphen-2 indicated that p.ile563val was predicted to be damaging, disease causing, and probably damaging to and causing ldb3 dysfunction. as such, this mutation produces novel protein coding transcripts, which might explain the mfm phenotype in the patient. introduction myofibrillar myopathy (mfm) is a rare human disease, cha...

Journal: :Proceedings of the National Academy of Sciences 1941

مروتی, سعید, ناصری, فرنوش,

Dentinogenesis imperfecta (DI) is an inherited disorder affecting dentin. Defective dentin formation results in discolored teeth that are prone to attrition and fracture. Mutation in dentin and the main gene in this disease is DSPP. Heterozygous mutations in this gene cause tooth sialophosphoprotein (DSPP) causes dentin disorders DI I and II. Imperfecta is a dominant autosomal trait that affec...

Abolfazl Akbari, Fariba Ghassemi Ghasem Fakhraie, Mansour Heidari, Masoumeh Mohebi, Mehran Zarei-Ghanavati Nahid Babaie Saeed Chenari,

Objective(s): Childhood cataract is a genetically heterogeneous eye disorder that results in visual impairment. The aim of this study was to identify the genetic mutations of connexin 50 gene among Iranian families suffered from autosomal dominant congenital cataracts (ADCC). Materials and Methods: Families, having at least two members with bilateral familial congenital cataract, were selected ...

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