نتایج جستجو برای: penetrant agent

تعداد نتایج: 254784  

Journal: :Proceedings of the National Academy of Sciences of the United States of America 1988
B Newman M A Austin M Lee M C King

Segregation analysis of breast cancer in families can provide the logical basis and the specific genetic models for mapping and identifying genes responsible for human breast cancer. Patterns of breast cancer occurrence in families were investigated by complex segregation analysis. In a sample of 1579 nuclear families ascertained through a population-based series of probands, an autosomal domin...

Journal: :Frontiers in bioscience : a journal and virtual library 2006
Ann W Hsing Anand P Chokkalingam

Prostate cancer is the most common non-skin cancer among men in most western populations, and it is the second leading cause of cancer death among U.S. men. Despite its high morbidity, the etiology of prostate cancer remains largely unknown. Advancing age, race, and a family history of prostate cancer are the only established risk factors. Many putative risk factors, including androgens, diet, ...

Journal: :Neuromuscular disorders : NMD 2004
M M O Tonini M R Passos-Bueno A Cerqueira S R Matioli R Pavanello M Zatz

Facioscapulohumeral muscular dystrophy is an autosomal dominant muscle disorder, mapped to 4q35. It is characterized by remarkable inter- and intrafamilial clinical variability ranging from severe phenotype to asymptomatic carriers. The aim of the present study was to assess the size of the Eco RI fragment in a large sample of asymptomatic or minimally affected carriers as well as symptomatic p...

2013
Francesco Berardinelli Alessandra di Masi Antonio Antoccia

The relationship between DNA repair failure and cancer is well established as in the case of rare, high penetrant genes in high cancer risk families. Beside this, in the last two decades, several studies have investigated a possible association between low penetrant polymorphic variants in genes devoted to DNA repair pathways and risk for developing cancer. This relationship would be also suppo...

2014
ANNA ROHLIN THEOFANIS ZAGORAS STAFFAN NILSSON ULF LUNDSTAM JAN WAHLSTRÖM LEIF HULTÉN TOMMY MARTINSSON GÖRAN B. KARLSSON MARGARETA NORDLING

Somatic mutations in the POLE gene encoding the catalytic subunit of DNA polymerase ε have been found in sporadic colorectal cancers (CRCs) and are most likely of importance in tumour development and/or progression. Recently, families with dominantly inherited colorectal adenomas and colorectal cancer were shown to have a causative heterozygous germline mutation in the proofreading exonuclease ...

2010
Andrea Romano Marleen Baars Herman Martens Rita Brandao Yvonne Detisch Eveline Jongen Marinus J. Blok Patrick Lindsey Encarna B. Gómez García

More than 50% of the families with BC and OC do not have mutations in the BRCA1 and BRCA2 genes [1-4]. So far, linkage analyses have failed in identifying new high penetrant genetic risk-factors responsible for the familial aggregation of those malignancies. It is hypothesized that the genetic basis in the remaining cases is highly heterogeneous [3-6] and that genes involved are low penetrant s...

2012
Puya Gharahkhani Caroline O’Leary David Duffy Michael Bernays Myat Kyaw-Tanner Jack Russell

Primary Lens Luxation (PLL) is an inherited disease common in Terrier breeds. A truncating mutation in the ADAMTS17 orthologue on CFA03 is reported to cause PLL in 17 breeds, mostly Terriers. This study investigated the mode of inheritance and penetrance of PLL, age of the ADAMTS17 mutation, and other possible causes of PLL in Australian Tenterfield Terriers and Miniature Bull Terriers. The ADA...

2015
A Mesut Erzurumluoglu Santiago Rodriguez Hashem A Shihab Denis Baird Tom G Richardson Ian N M Day Tom R Gaunt

Recent technological advances have created challenges for geneticists and a need to adapt to a wide range of new bioinformatics tools and an expanding wealth of publicly available data (e.g., mutation databases, and software). This wide range of methods and a diversity of file formats used in sequence analysis is a significant issue, with a considerable amount of time spent before anyone can ev...

2016
Maria-Carmela Speranza Michal O. Nowicki Prajna Behera Choi-Fong Cho E. Antonio Chiocca Sean E. Lawler

Glioblastoma is an aggressive, invasive tumor of the central nervous system (CNS). There is a widely acknowledged need for anti-invasive therapeutics to limit glioblastoma invasion. BKM-120 is a CNS-penetrant pan-class I phosphatidyl-inositol-3 kinase (PI3K) inhibitor in clinical trials for solid tumors, including glioblastoma. We observed that BKM-120 has potent anti-invasive effects in gliobl...

2011
Lisenka E. L. M. Vissers Timothy C. Cox A. Murat Maga Kieran M. Short Fenny Wiradjaja Irene M. Janssen Fernanda Jehee Debora Bertola Jia Liu Garima Yagnik Kiyotoshi Sekiguchi Daiji Kiyozumi Hans van Bokhoven Carlo Marcelis Michael L. Cunningham Peter J. Anderson Simeon A. Boyadjiev Maria Rita Passos-Bueno Joris A. Veltman Ian Smyth Michael F. Buckley Tony Roscioli

The premature fusion of the paired frontal bones results in metopic craniosynostosis (MC) and gives rise to the clinical phenotype of trigonocephaly. Deletions of chromosome 9p22.3 are well described as a cause of MC with variably penetrant midface hypoplasia. In order to identify the gene responsible for the trigonocephaly component of the 9p22.3 syndrome, a cohort of 109 patients were assesse...

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