Klippel-Trénaunay syndrome (KTS) is an uncommon entity. This congenital malformation is characterized by the triad of soft tissue or bony hypertrophy, cutaneous vascular malformations, and atypical venous abnormalities. We report here a case of KTS and discuss the clinical features, investigations, and management of this enigmatic condition.

Cerebral cavernous malformation (CCM) is a disease of vascular malformations known to be caused by mutations in one of three genes: CCM1, CCM2 or CCM3. Despite several studies, the mechanism of CCM lesion onset remains unclear. Using a Ccm1 knockout mouse model, we studied the morphogenesis of early lesion formation in the retina in order to provide insight into potential mechanisms. We demonst...

Sir, Selective embolization is used pre-operatively for highly vascular tumours, for treatment of vascular malformations and for treatment of bleeding. The morbidity rate of this technique is less than 1% (1, 2). Skin necrosis is described as an uncommon and minor adverse e¡ect.We present a case of cicatricial alopecia following intravascular embolization for incoercible bleeding of the nose.

VENOUS VASCULAR MALFORMATION OF LIP – A CASE REPORT Vijayparthiban Sethuraman, 1 Sriram Kaliamoorthy, 2 Semmia Mathivanan, 3 Aesha Imran 4 1. Reader, Department of Oral & Maxillofacial Suregry, Chettinad Dental College & Research Institute, Tamilnadu 2. Senior lecturer, Department of Oral Pathology & Microbiology, Chettinad Dental College & Research Institute, Tamilnadu 3. Senior lecturer, Depa...

Vascular malformations are rare congenital lesions which often have associated skeletal changes. Over a period of ten years, 90 patients at our clinic had a vascular anomaly of the lower limb, examined by either CT or MRI. Of these, 18 (20%) had bony involvement. A questionnaire was sent to these patients (8 men, 10 women) to evaluate their age of presentation, initial symptoms and current comp...

We revised 16 patients submitted to epilepsy surgery using a new method of digital, real-time, portable electrocorticography. Patients were operated upon over a period of 28 months. There were no complications. The exam was useful in 13 cases. The low installation and operational costs, the reliability and simplicity of the method, indicate it may be useful for defining the epileptogenic region...

Vascular anomalies comprise a heterogeneous group of disorders that are divided into tumors (hemangiomas) and malformations. Recent advances in biomedical research provide insights into the molecular basis of these disorders and a deeper understanding of vascular morphogenesis. In the future, this emerging knowledge will contribute to novel ways to treat vascular anomalies and to regulate patho...

Identification and treatment of vascular malformations is a challenging endeavor for physicians, especially given the great concern and anxiety created for patients and their families. The goal of this article is to provide a review of vascular malformations, organized by subtype, including capillary, venous, lymphatic and arteriovenous malformations. Only by developing a clear understanding of...

congenital, but are of most interest because of their potentially malignant nature, and are therefore classified as malignant tumors. Certain other discrepancies in classification may be noted. Hamartomas, for instance, have included only the chondromata, although, as described by Albrecht,’ this designation might apply to any tissue indigenous to the area forming a mass, and would therefore in...