BACKGROUND Double outlet right ventricle (DORV), a clinically significant congenital heart defect, occurs in 1-3% of individuals with congenital heart defects. In contrast to other major congenital heart defects, there are no systematic or comprehensive data regarding associations, aetiologies, and pathogenesis of DORV. We analysed reported cases in the medical literature to address these issue...

The entity of double outlet right ventricle is being increasingly recognized in recent years (Neufeld, DuShane, and Edwards, 1961a; Neufeld et al., 1961b, 1962; Morgan et al., 1962; Mehrizi, 1965; Venables and Campbell, 1966). The oldest patient in the series reported by Mehrizi (1965) was 22 years and in the 10 patients of Venables and Campbell (1966) the oldest was 9 years. We report a patien...

ABSENCE of the pulmonic valve is a rare congenital lesion which is usually associated with tetralogy of Fallot." 2 We have recently observed a patient in whom this anomaly coexisted with "double-outlet right ventricle." This case is reported because a review of the literature has failed to reveal a similar case and because certain difficulties inherent in the differentiation of double-outlet ri...

the present report describes a male newborn with a pulsatile structure beneath the sternum. echocardiography showed common atrium, a single ventricle, mitral atresia, double outlet right ventricle, subpulmonary stenosis, small pulmonary artery branches, and a thin walled ventricular diverticulum suggestive of cantrell's syndrome. the diverticulum was resected to prevent life threatening events ...

The results of complete repair of double-outlet right ventricle with pulmonic stenosis in 22 Mayo Clinic patients were analyzed. The overall mortality rate was 32%. Since 1960, the mortality rate has been reduced to 16%. Anomalies of the distribution of the right coronary artery, a second ventricular septal defect of the atrioventricular canal type, and significant residual pulmonic stenosis we...

Double outlet right ventricle, a rare congenital heart anomaly of either animals or man, was diagnosed in a three day old Brangus heifer. The clinical course was brief, consisting of terminal recumbency, dyspnea and cyanosis. Upon necropsy, the heart was enlarged as a result of marked dilatation of the right atrium and the right ventricle. The aorta arose from the right ventricle while the left...

Although transposition of the great vessels is a well-known clinical and pathological entity, the partial transposition complex, resulting in the origin of both the aorta and the pulmonary trunk from the right ventricle, is rare. The association of this malformation with pulmonary stenosis has been described previously (Braun et al., 1952; Witham, 1957; Neufeld, DuShane, and Edwards, 1961; Morg...

Double Outlet Right Ventricle with intact ventricular septum is an extremely rare malformation. Only nine cases are recorded in the known world literature. A new case is reported, concerning a female infant six months old when first seen, and still alive after atrial septectomy. The anatomical studies in Double Outlet Right Ventricle suggest that only the Ventricular Septal Defect in the outlet...

Carpenter syndrome (Acrocephalopolysyndactyly type 2, OMIM 201000) is a rarely seen autosomal recessive disorder. In addition to abnormalities such as acrocephaly, craniosynostosis, facial asymmetry, polydactyly and syndactyly, obesity, hypogonadism, mental retardation, and corneal opacity, it may frequently be accompanied by congenital heart diseases such as ventricular septal defect, patent d...

Background/Introduction Anomalies of ventriculoarterial connection with ventricular septal defect (VSD) and left ventricular outflow tract (LVOT) obstruction such as transposition of the great arteries, double-outlet right ventricle, double-outlet left ventricle, and Taussig-Bing anomaly had a wide variety of spectrum, and several operative techniques have been performed according to diverse an...