intracranial lipomas are congenital malformations. these uncommon lesions have an incidence of 0.1 to 1.7% of all intracranial tumors. most cases are located at midline and 5% are along the sylvian fissures. if symptomatic, seizures are the most common symptom. these tumors are slow growing and have favorable outcome. we report a case of a 25-year-old man whose ct and mri revealed a lesion in r...

dysplasia epiphysealis hemimelica is a rare nonhereditary epiphyseal disease that mimics synovial chondromatosis and osteochondroma of the joints. the disease mainly involves long bones of the lower extremities and tarsal bones. herein we report 21-year old woman who presented with pain and limited range of ankle motion, who underwent surgical excision of talus exostosis after preoperative imag...

alveolar ridge is underdeveloped in ectodermal dysplasia (ed). the available treatment plans include fixed, removable or implant-supported prostheses, alone or in combination. a 5 year-old boy was referred for treatment to the department of prosthodontics, tehran university of medical sciences with the chief complaint of missing teeth. prosthodontic treatment was performed to improve masticatio...

Introduction: Dentin dysplasia is a rare autosomal dominant inheriting disturbance of dentin formation characterized by normal enamel formation, but atypical dentin with abnormal pulpal morphology. There are two major patterns: type I and type II. Amelogenesis imperfecta is an autosomal dominant. X-link inherent disease that is classified by clinical manifestation into hypoplastic, hyp...

dentin dysplasia is an exceptionally rare, autosomal-dominant, hereditary condition, primarily characterized by defective dentin formation affecting both the deciduous and permanent dentitions. the etiology remains imprecise to date, in spite of the numerous hypotheses put forward and the constant updates on this condition. this case report of type i dentin dysplasia exhibits radiographic fi nd...

developmental dysplasia of the hip (ddh) or congenital hip dysplasia (cdh) is the most prevalent developmental childhood hip disorder. it includes a wide spectrum of hip abnormalities ranging from dysplasia to subluxation and complete dislocation of the hip joint. the natural history of neglected ddh in adults is highly variable. the mean age of onset of symptoms is 34.5 years for dysplastic dd...

objective: florid cemento-osseous dysplasia (fcod) is a rare bone lesion that predominantly involves the women’s jaws in middle age. this condition is usually asymptomatic and has a benign course.   case: this paper presents a rare case of fcod in a white middle aged woman, which had affected mandible bilaterally and was diagnosed after tooth extraction and treated conservatively.   we believed...

fibrous dysplasia (fd) is an osseous growth dis-order, producing immature bone and characte-rized by the replacement of normal bone with fibro-osseous connective tissue. it is a bone dys-plasia that has the potential to cause significant cosmetic and functional disturbances, particularly in the craniofacial skeleton. cra-niofacial fibrous dysplasia is one of the three types of polyostotic fibro...