نتایج جستجو برای: amplified refractory mutation system

تعداد نتایج: 2553865  

Background The X-linked cyclin-dependent kinase like 5 (CDKL5/STK9) gene has been shown to be responsible for a severe encephalopathy condition characterized by early onset of epilepsy and severe developmental delay. CDKL5 mutations have been shown to be more frequent among female patients. Results Here we report a 6- month male patient, second child of a healthy non consanguineous in the Irani...

ابهجی, مریم, اسمیت, ریچارد, بزاز زادگان, نیلوفر, جوان, محمد خلیل, خدایی, حسین, دهقانی, عاطفه, ریاض الحسینی, یاسر, سیفتی, مرتضی, مغنی باشی, مهدی, میراب, محمود, نجم آبادی, حسین, کهریزی, کیمیا,

Introduction: Hearing loss is the most common sensory neural defect in humans, affecting 1 in 1000 neonates, with over half of these cases predicted to be hereditary in nature. Most hereditary hearing loss is inherited in a recessive fashion, accounting for approximately 80 % of non-syndromic hearing loss (NSHL). Mutations in GJB2 gene are major cause of inherited deafness in the European an...

Journal: :Journal of medical genetics 1994
M Ali G Tunçman N C Cross M Vidailhet I Bökesoy R Gitzelmann T M Cox

We report three new mutations in the gene for aldolase B that are associated with hereditary fructose intolerance (HFI). Two nonsense mutations create opal termination codons: R3op (C-->T, Arg3-->ter, exon 2) was found in homozygous form in four affected members of a large consanguineous Turkish pedigree and R59op (C-->T, Arg59-->ter, exon 3) was found on one allele in a woman of Austrian origi...

Journal: :iranian journal of allergy, asthma and immunology 0
reza alibakhshi mahdi zamani

cystic fibrosis (cf) is the most common inherited disorder in caucasian populations, with over 1400 cystic fibrosis transmembrane conductance regulator (cftr) mutations. the type of mutations and their distributions varies widely between different countries and/or ethnic groups. seventy iranian cystic fibrosis patients were screened for the cftr gene mutation using arms/pcr (amplification refra...

Journal: :Revista da Sociedade Brasileira de Medicina Tropical 2012
Laynara Katize Grutzmacher Eduardo Monguilhott Dalmarco Solange Lucia Blatt Caio Mauricio Mendes de Cordova

INTRODUCTION The aim of this work was to evaluate the prevalence of Mycobacterium tuberculosis (MT) strains with mutations that could result in resistance to the main drugs used in treatment in a region with one of the highest numbers of tuberculosis (TB) cases in southern Brazil. METHODS Deoxyribonucleic acid (DNA) from 120 sputum samples from different patients suspicious of pulmonary tuber...

Journal: :OncoTargets and therapy 2016
Miaomiao Wen Xuejiao Wang Ying Sun Jinghua Xia Liangbo Fan Hao Xing Zhipei Zhang Xiaofei Li

PURPOSE Echinoderm microtubule-associated protein-like 4-anaplastic lymphoma kinase (EML4-ALK) and epidermal growth factor receptor (EGFR) define specific molecular subsets of lung cancer with distinct clinical features. We aimed at revealing the clinical features of EML4-ALK fusion gene and EGFR mutation in non-small-cell lung cancer (NSCLC). METHODS We enrolled 694 Chinese patients with NSC...

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