Segmental neurofibromatosis (SNF) is a rare variant of neurofibromatosis (NF) type 1 characterized by a restricted distribution of cafe-au-lait macules, and/or neurofibromas, and rarely freckling to a single dermatomal segment. Patients with NF type 1 have an associated increased risk for benign or malignant tumours. The prevalence of typical NF type 1 complications including malignancies in SN...

We present a 7-year-old girl with no past history of interest, who was seen for an asymptomatic lesion that had arisen in the right axilla 3 months earlier and had grown progressively, but that had remained stable after a cycle of cryotherapy in her health center 2 months earlier. Examination revealed a well-defined oval papule in the right axilla. The papule was of yellowish color centrally an...

We present a 7-year-old girl with no past history of interest, who was seen for an asymptomatic lesion that had arisen in the right axilla 3 months earlier and had grown progressively, but that had remained stable after a cycle of cryotherapy in her health center 2 months earlier. Examination revealed a well-defined oval papule in the right axilla. The papule was of yellowish color centrally an...

Eruptive vellus hair cysts are disorders that present as cystic papules usually on the chest and extremities. Facial involvement is very rare in this disorder and few reports of facial eruptive vellus hair cysts have been presented till now.We present two cases of eruptive vellus hair cysts in a mother and her daughter with facial distribution.

efficacy. These lesions are rarely selflimiting, and recurrences are common. We describe a 25-year-old woman with no relevant history who consulted for asymptomatic, flesh-colored papules of 1-2 mm, distributed on the anterior area of the neck and neckline (Figure 1). The symptoms started 10 years earlier on the lower eyelids, gradually spreading to the abdomen, neck, and neckline, with outbrea...

cells of the mononuclear phagocyte system and the dendritic system(l). Each of the histiocytoses of childhood is characterized by localized or generalized, reactive or neoplastic proliferation of cells similar if not identical to one of these cell types(2). As per Writing Group of the Histiocyte Society(3), various histiocytoses of childhood have been classified into Class I, Class II and Class...

langerhans cell histiocytosis (lch) is a rare disorder described as three different entities including eosinophilic granulomaof bone, the hand-schuller-christian syndrome, and letterer-siwe disease. lch is currently classified into singlesystem lch, and multisystem lch. patients with single system lch have an excellent prognosis, and are mostlytreated with local therapy. multisystem lch is subd...