The Dyke-Davidoff-Masson Syndrome (DDMS) results from an insult to the growing brain in utero or early infancy, which lead to loss of neurons compromising the growth of the brain. Clinical presentation includes seizures, hemiparesis, facial asymmetry, and learning disability. Radiological findings include cerebral atrophy on one side. Here, we present a case with status epilepticus who had unde...

Acta Neurologica Taiwanica Vol 19 No 2 June 2010 From the Department of Neurology, National Taiwan University Hospital Yun-Lin Branch, Yunlin, Taiwan. Received October 27, 2009. Accepted November 9, 2009. Reprint requests and correspondence to: Fu-Yu Lin, M.D. Department of Neurology, National Taiwan University Hospital Yun-Lin Branch, No. 579, Sec. 2, Yunlin Rd., Douliou City, Yunlin, Taiwan. ...

We read a case report by Manghera et al (JAPI, Vol 62 page No. 76-67), which was in response to an earlier case report by Ola et al.1 Here we would like to share our experience and views as under- The authors in the correspondence have said that crossed cerebellar atrophy is an unusual and rare finding. We in our study of 28 patients of DDMS, have found cerebellar atrophy in nine patients along...

UNLABELLED Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is...

Dyke-Davidoff-Masson syndrome (DDMS) is a rare disorder characterized by recurrent seizures, facial asymmetry, contralateral hemiplegia, radiologic features of cerebral hemiatrophy, and ipsilateral compensatory hypertrophy of the skull bone and sinuses. We describe three cases of children with DDMS, who initially presented with refractory seizure to the pediatric department of North Bengal Medi...

To cite: Anandpara KM, Aswani Y, Hira P. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2014206682 DESCRIPTION A 14-year-old girl, known case of seizure disorder since 10 years and mild mental retardation, presented with progressive left-sided hemiparesis and a recent increase in the frequency of seizures. Significant history included a developmental lag. A CT of...