Dyke Davidoff Masson syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. The characteristic radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. We report a case of DDMS in an 18-month-old girl who presented with right sided focal seizures, hemiparesis of the same side, and delayed milest...

Dyke-Davidoff-Masson syndrome refers to atrophy of one cerebral hemisphere (hemiatrophy) due to an insult to the brain in fetal or early childhood period. This is an uncommon condition. We present a case of a nine month- old female presented with seizure and weakness of the right upper and lower extremities and subsequently computed tomography was performed and showed hemiatrophy of the left fr...

Refractory epilepsy is common in practice of neurology. Dyke-Davidoff-Masson Syndrome (DDMS) is one among the syndromes associated with refractory epilepsy. We have come across a case of Dyke-Davidoff-Masson syndrome while investigating a case of refractory epilepsy. When cerebral hemi atrophy is associated with the radiological features of osseous hypertrophy of calvarium, hyper-pneumatisation...

DESCRIPTION An 18-month-old baby presented with decreased movements of right upper and lower limb since birth. The birth history revealed perinatal insult in the form of delayed cry that was followed by right-sided complex partial seizures. The patient exhibited delayed milestones. There is no history of cyanosis, jaundice or head injury in the neonatal period. At present, the patient is unable...

Dyke-Davidoff-Masson Syndrome (DDMS) is a rare syndrome characterized with specific clinical and radiological findings due to involvement of the developing brain cerebral hemiatrophy one hemisphere. The was first described from Dyke, Davidoff Masson in 1933 series nine patients. has two forms, congenital acquired forms etiological factors vary brain. Most common symptom are focal or secondary g...

the right side. All the findings favoured diagnosis of Dyke David -Masson syndrome. Significant contrasting feature in our patient than the patient described in the journal was the presence of left sided cerebellar atrophy (Figure 1). DykeDavidoff-Masson syndrome associated with crossed cerebellar atrophy (CCA) has been previously described in some pat ients . There are two schools of thought r...

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Dyke-Davidoff-Masson syndrome (DDMS) is a rare, but important cause of drug-resistant seizures. Dyke-Davidoff-Masson syndrome is a constellation of clinical features that consists of hemiparesis, seizure, facial asymmetry, and intellectual disability with distinct neuroimaging features. A 27-year-old lady presented to us with drug-resistant epilepsy, hemiparesis, and intellectual disability tha...