نتایج جستجو برای: prp gene

تعداد نتایج: 1146211  

Journal: :Folia neuropathologica 2004
Jolanta Bratosiewicz-Wasik Tomasz J Wasik Paweł P Liberski

Prion diseases such as scrapie in sheep, bovine spongiform encephalopathy in cattle, Creutzfeldt-Jakob disease, Gerstmann-Sträussler-Scheinker disease and fatal familial insomnia in man are neurodegenerative disorders. In humans, the diseases can be sporadic, inherited, or acquired by infection. The underlying pathogenic event in prion diseases is a conformational modification of the cellular i...

Journal: :Proceedings of the National Academy of Sciences of the United States of America 2006
Ranjit K Giri Rebecca Young Rose Pitstick Stephen J DeArmond Stanley B Prusiner George A Carlson

Only a few cell lines have been infected with prions, offering limited genetic diversity and sensitivity to several strains. Here we report that cultured neurospheres expressing cellular prion protein (PrP(C)) can be infected with prions. Neurosphere lines isolated from the brains of mice at embryonic day 13-15 grow as aggregates and contain CNS stem cells. We produced neurosphere cultures from...

2013
Xiangzhu Xiao Ignazio Cali Zhiqian Dong Gianfranco Puoti Jue Yuan Liuting Qing Heming Wang Qingzhong Kong Pierluigi Gambetti Wen-Quan Zou

Insertion of 144-base pair (bp) containing six extra octapeptide repeats between residues 51 and 91 of prion protein (PrP) gene is associated with inherited prion diseases. Most cases linked to this insertion examined by Western blotting showed detectable proteinase K-resistant PrPSc (rPrPSc) resembling PrPSc type 1 and type 2 in sporadic Creutzfeldt-Jakob disease (sCJD), or PrP7-8 in Gerstmann...

پایان نامه :وزارت علوم، تحقیقات و فناوری - دانشگاه تربیت مدرس - دانشکده پزشکی 1390

هموفیلوس آنفلوانزا تیپ b، نوعی باکتری گرم منفی کپسولدار است و یکی از شایع ترین عوامل مولد مننژیت حاد بشمار می آید. کپسول پلی ساکاریدی این باکتری ؛پلی ریبوزیل ریبیتول فسفات (prp )و پروتئین غشاء خارجی p6 به عنوان ایمونوژن در تولید واکسن علیه هموفیلوس آنفلوانزا نقش دارند .هدف از انجام این مطالعه ، کونژوگه نمودن پروتئین نوترکیب p6(rp6 ) با prp و ارزیابی ایمونولوژیک آن به عنوان کاندیدای جدید واکسینا...

Journal: :The EMBO journal 2005
Karah E Nazor Franziska Kuhn Tanya Seward Mike Green Daniel Zwald Mario Pürro Jaqueline Schmid Karin Biffiger Aisling M Power Bruno Oesch Alex J Raeber Glenn C Telling

The absence of infectivity-associated, protease-resistant prion protein (PrP(Sc)) in the brains of spontaneously sick transgenic (Tg) mice overexpressing PrP linked to Gerstmann-Sträussler Scheinker syndrome, and the failure of gene-targeted mice expressing such PrP to develop disease spontaneously, challenged the concept that mutant PrP expression led to spontaneous prion production. Here, we ...

2015
Agnese De Mario Angela Castellani Caterina Peggion Maria Lina Massimino Dmitry Lim Andrew F. Hill M. Catia Sorgato Alessandro Bertoli

The prion protein (PrP(C)) is a cell surface glycoprotein mainly expressed in neurons, whose misfolded isoforms generate the prion responsible for incurable neurodegenerative disorders. Whereas PrP(C) involvement in prion propagation is well established, PrP(C) physiological function is still enigmatic despite suggestions that it could act in cell signal transduction by modulating phosphorylati...

2013
Julie Nemecek Nabanita Nag Christina M. Carlson Jay R. Schneider Dennis M. Heisey Christopher J. Johnson David M. Asher Luisa Gregori

Rapid antemortem tests to detect individuals with transmissible spongiform encephalopathies (TSE) would contribute to public health. We investigated a technique known as protein misfolding cyclic amplification (PMCA) to amplify abnormal prion protein (PrP(TSE)) from highly diluted variant Creutzfeldt-Jakob disease (vCJD)-infected human and macaque brain homogenates, seeking to improve the rapid...

Journal: :The Journal of general virology 2008
Gültekin Tamgüney Kurt Giles David V Glidden Pierre Lessard Holger Wille Patrick Tremblay Darlene F Groth Fruma Yehiely Carsten Korth Richard C Moore Jörg Tatzelt Eric Rubinstein Claude Boucheix Xiaoping Yang Pamela Stanley Michael P Lisanti Raymond A Dwek Pauline M Rudd Jackob Moskovitz Charles J Epstein Tracey Dawson Cruz William A Kuziel Nobuyo Maeda Jan Sap Karen Hsiao Ashe George A Carlson Ina Tesseur Tony Wyss-Coray Lennart Mucke Karl H Weisgraber Robert W Mahley Fred E Cohen Stanley B Prusiner

Prion diseases are caused by conversion of a normally folded, non-pathogenic isoform of the prion protein (PrP(C)) to a misfolded, pathogenic isoform (PrP(Sc)). Prion inoculation experiments in mice expressing homologous PrP(C) molecules on different genetic backgrounds displayed different incubation times, indicating that the conversion reaction may be influenced by other gene products. To ide...

Journal: :Journal of virology 2002
Alana M Thackray Raymond Bujdoso

PrP(c) is a glycophosphatidylinositol-linked cell-surface protein expressed principally by neural tissue. The normal function of this protein is unestablished, although a role in either transmembrane signaling, cell-cell adhesion, or copper metabolism has been proposed. In this study we have investigated the effect of the neurotropic virus herpes simplex virus type 1 (HSV-1) in strains of mice ...

Journal: :The American journal of sports medicine 2011
Gerben M van Buul Wendy L M Koevoet Nicole Kops P Koen Bos Jan A N Verhaar Harrie Weinans Monique R Bernsen Gerjo J V M van Osch

BACKGROUND Platelet-rich plasma (PRP) has recently been postulated as a treatment for osteoarthritis (OA). Although anabolic effects of PRP on chondrocytes are well documented, no reports are known addressing effects on cartilage degeneration. Since OA is characterized by a catabolic and inflammatory joint environment, the authors investigated whether PRP was able to counteract the effects of s...

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