alport syndrome is a progressive hereditary nephritis leading to renal failure. nearly all of the documents declare that alport syndrome is inherited as x-linked dominant trait and reports of autosomal inheritance form is very rare. this paper presents an iranian large alport family with autosomal recessive inheritance. in our patients alport disease was confirmed with electron microscopic stud...

• AbstractThis research was done to provide effective strategies for the establishment of integration model for succession planning and career progression path of azad universities administrators from the perspective of higher education administrators and professionals based on the systematic theoretical design of Strauss and Corbin grounded theory. Accordingly, using a targeted sampling method...

It is a privilege to begin my term as editor-in-chief of the British Journal Ophthalmology ( BJO ), and with benefit number significant improvements made journal over past seven years by outgoing editors-in-chief, Keith Barton, James Chodosh Jost Jonas. Their stewardship has been successful every measure. My responsibility for next further expand quality standing . In this I will not be alone. ...

A new test of inheritance, S, is proposed, which uses information from affected as well as unaffected siblings in the fam­ ily. The siblings are analyzed in terms of similarities of haplotypes. The distribution of the proposed S­test is derived under the null hypothesis of random inheritance. Mean and variance are obtained for the distribution. The test is then applied to data sets publ...

This paper discusses the innovativeness of Inheritance Ordinance introduced in Toledo during 12th century and later reintroduced Fez Morocco following expulsion Jewish communities from Spain Portugal. Community leaders Toledo, after also Fes, transformed laws succession established biblical times by granting women equal rights on matters inheritance marriage. The ordinance granted unmarried dau...

arguing that human rights treaties by their nature are different from other international agreements, this article deals mainly with such questions as succession of states in respect of human rights treaties and reservations to such instruments.  in contrast to other treaties, which are generally “inter-states exchange of interests”, human rights documents are protective instruments according t...

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In this paper we assess the relationship between how women access land they farm, and their farming identities, roles, future succession plans. Utilizing a Bourdieusian approach, conceptualize inheritance of farmland as long-term process symbolic economic investment. We conducted cohort analysis living or working on farms in Scotland, UK who (a) were not raised farms; (b) bought into inherited ...