Until recently the outlook for neonates with distal tracheal stenosis was uniformly poor, but several reports 1-4 have suggested that tracheal resection may be performed successfully in infants with this condition. We report the case of an infant who underwent surgery for double aortic arch and subsequently required resection of the distal trachea because of localised tracheomalacia. In contras...

Three cases of Wilms' tumour and sporadic aniridia were followed up for periods ranging from 32 months to seven years. All had a deletion of the short arm of the eleventh chromosome 11p13, including one case with mosaicism, a cytogenetic feature that has not been previously described in the Wilms' tumour and sporadic aniridia association. Unusual non-ocular features found in all patients includ...

Results: A total of 54 patients underwent MDO and of those 21 patients were found who have undergone both MDO and DLB. The incidence of at least 1 SAL was 71.4% in this group. A subgroup of patients less than 24 months had an incidence of SALs that was 78%. Types of SALs encountered include laryngeal edema (57.1%), tracheobronchitis (42.9%), laryngomalacia (33.3%), tracheomalacia (14.3%), bronc...

Mounier-Kuhn Syndrome (MKS) is a rare congenital disease that presents with abnormal enlargement in the central airways. In MKS, tracheomegaly is accompanied by difficulty in expelling recurrent lung infections and bronchiectasia. We presented a patient with MKS where commercially made stents were inadequate for stabilization and a custom-made, self-expandable metallic stent with a diameter of ...

Patients with Morquio syndrome can develop respiratory failure secondary to reduced chest wall compliance and airway collapse from irregularly shaped vocal cords and trachea. We report the case of a patient with Morquio syndrome whose clinical course was complicated by tracheomalacia. An obese 29-year-old female with Morquio syndrome presented with severe wheezing and tachycardia. One month pri...

OBJECTIVE We conducted a retrospective study to determine the relationship between gastroesophageal reflux (GER) and large airways malacia in infancy. METHODS One hundred sixteen children referred for chronic respiratory problems who were between the ages of 3 and 28 months were investigated. All of them underwent flexible bronchoscopy and chest radiography. Eighteen children had laryngomalac...