idiopathic lobular panniculitis, sometimes called relapsing febrile nodular panniculitis or weber christian disease first desribed in 1892 by pfeifer, is the term used to describe an group of disease that present as subcutaneous inflammatory nodules and histologically display an inflammatory focus primarily within the fat lobules. weber-christian disease is the term applied to idiopatic cases o...

Weber Christian disease or idiopathic lobular panniculitis is a skin condition that features recurring inflammation in the fat layer of the skin. We report a case of a 17 year old boy with Weber Christian disease as its occurence is extremely rare with only sparse case reports available, who presented with eighteen-month history off fever with chills off and on, arthralgia predominantly of the ...

BACKGROUND Weber-Christian disease is a controversial entity that histologically presents as a lobular panniculitis. A systemic variant of this disorder, in which visceral fat is affected, has been reported. OBJECTIVE A 29-year-old woman with Weber-Christian disease developed a rapidly enlarging abdominal mass during hospitalization for a flare of her skin condition. The mass resolved spontan...

SYNOPSIS A patient suffering from Weber-Christian panniculitis was found at necropsy to have similar lesions in the visceral adipose tissue. When the lesions occur internally, diagnosis during life is complicated by the difficulty of examining visceral adipose tissue and the disease may often go unrecognized, but patients suffering from Weber-Christian panniculitis should be investigated bearin...

ENDOCRINOLOGICAL, METABOLIC DISORDERS hypophysis dysfunction diabetes insipidus GENITAL DISORDERS genital dysfunctions puberty, delayed HEMOPOIETIC-LYMPHORETICULAR SYSTEM DISORDERS lymphonodus disorders lymphonodus enlarged, lymphadenopathy spleen, anomalies splenomegaly, hepatosplenomegaly LABORATORY DATA lymphoreticular system, changes histiocytosis, including histiocytoma myelo-erythropoieti...

In 1948 Ormond reported two cases of unheralded anuria due to idiopathic retroperitoneal fibrosis. Previous documentation of the condition had been scanty, but since then over a hundred similar cases have been reported. The patient, usually an adult, at first has only vague symptoms such as abdominal discomfort, anorexia, loss of weight, or nausea. The diagnosis is made usually only when signs ...

A fourteen month old infant was admitted for evaluation because of continuous high fever and an indurated nodular lesion at the left thigh of one month course. After admittance painful inflammatory subcutaneous nodules appeared in the face and trunk, these were accompanied by enlarged cervical lymph nodes and hepatomegaly. Histological evaluation of the skin biopsy showed destruction of subcuta...

It has been proposed that idiopathic retroperitoneal fibrosis may be a consequence of 'healed' retroperitoneal lesions of systemic Weber-Christian disease. However ureteric obstruction which is the hallmark of idiopathic retroperitoneal fibrosis, has not been described in systemic Weber-Christian disease. We report a patient with systemic Weber-Christian disease who, during a relapse, developed...

Weber Christian disease, an idiopathic relapsing febrile subcutaneous and visceral panniculitis is a rare disease in children. We report a case of Weber Christian disease for he first time from Kanti Children's Hospital.