primary immunodeficiency diseases (pids) are rare but include severe conditions found predominantly in children, most pids have cutaneous manifestations that may be important as early diagnostic features. the purpose of this study was to determine the frequency and nature of cutaneous alterations associated with pids. this article is a cross-sectional study at the department of allergy and clin...

Lymphadenopathy refers to any disease process involving lymph nodes that are abnormal in size and consistency. Lymphadenitis specifically refers to lymphadenopathies that are caused by inflammatory processes. Cervical lymphadenopathy is a common problem in the pediatric age group and is largely inflammatory and infectious in etiology. Although most patients are treated successfully by their pri...

Serum erythrepoietin (ESF) levels were An impaired ESF response in these infants measured by the polycythemic mouse may be an important factor in the pathsbioassay in a group of normal premature genesis of the anemia of prematurity. infants with physiologic anemia. No ESF Tissue oxygen requirements in the prewas detected in these infants, while a mature infant are probably met in some group of ...

Since heterozygous familial hypercholesterolemia (HeFH) is a disease that exposes the individual from birth onwards to severe hypercholesterolemia with the development of early cardiovascular disease, a clear consensus on the management of this disease in young patients is necessary. In Belgium, a panel of paediatricians, specialists in (adult) lipid management, general practitioners and repres...

ackground: Learned self-control of slow cortical potentials (SCPs) may lead to behavioral improvement in attention-deficit/ yperactivity disorder (ADHD). Hence, training effects should also be reflected at the neurophysiological level. ethods: Thirteen children with ADHD, aged 7–13 years, performed 25 SCP training sessions within 3 weeks. Before and after raining, the German ADHD rating scale w...

tenoses of multiple peripheral pulmonary artery branches represent a rare cause of pulmonary hypertension in hildren, but the prognosis is very poor for such patients. Herein we describe 2 patients with multiple peripheral ulmonary artery stenoses (MPPAS) presenting with severe pulmonary arterial hypertension in adulthood, which as only once been described previously. Both patients lived withou...

etralogy of Fallot with or without pulmonary atresia ccounts for approximately 10% of all forms of congenital eart disease. Establishing unobstructed blood flow between he right ventricle (RV) and the confluence of the pulmoary arteries using the transannular patch technique or via he insertion of an interposition graft valve between the RV nd pulmonary artery have been the main surgical option...

Screening of blood reduces but does not eliminate the risk of hepatitis B virus (HBV) infection in multi-transfused thalassaemia patients. This study was done to evaluate efficacy of HBV vaccination on hepatitis B virus surface antigen (HBsAg) carrier rate in children with thalassaemia major receiving multiple blood transfusions. In a cohort study conducted at a hospital in Bahawalpur, Pakistan...