Neurothekeoma is a rare cutaneous neoplasm, occurring as a cutaneous papule or nodule on the face, shoulders, and upper extremities. Neurothekeoma has been subclassified as either the myxoid, cellular, or mixed type, depending on the amount of myxoid matrix and on immunohistochemical analysis. We observed a clinical case with conflicting histopathological and immunohistochemical findings. In th...

Neurothekeoma is a benign nerve sheath tumor, also known as nerve sheath myxoma. It arises from the cutaneous nerves of the head and neck region. In certain cases, neurothekeoma has been reported in the breast, oral cavity, tongue, maxilla, and spinal intradural space. Intracranial neurothekeoma, however, is an extremely rare entity, with only three cases reported in the literature: one in the ...

32 ABSTRACT Benign nerve sheath myxoma (myxoid neurothekeoma) is a rare benign cutaneous neoplasm of nerve sheath origin. This tumor is commonly seen in the head and neck region and sometimes in the upper extremity. The presence of myxoid neurothekeoma on the lower limb is seldom and rarely reported. In this report we presented a new case of myxoid neurothekeoma in the lower limb of a 42-year-o...

Dear Editor, Neurothekeomas are rare benign dermal tumors, which originate from the peripheral nerve sheath. They are divided into myxoid, intermediate, and cellular types, based on the amount of myxoid matrix and on the immunohistochemical study. We report an unusual S-100 negative case of myxoid neurothekeoma, which is currently described in the literature as a new type of neurothekeoma. A 73...

Nerve sheath myxoma (neurothekeoma) are rare benign nerve sheath tumors, usually arising in the skin of the head and neck region and upper extremities in young females. To the best of author's knowledge only two cases of intracranial neurothekeoma have been published in the English literature. These tumors were located in the parasellar area and in middle cranial fossa. This is ...

Very recently, Requena et al. have demonstrated the detailed clinicopathological features of 9 cases of a benign cutaneous plexiform nerve sheath tumor with hybrid characteristics of perineurioma and cellular neurothekeoma, given the name as a benign cutaneous plexiform hybrid tumor of perineurioma and cellular neurothekeoma, all of which were peculiarly located on the lips. Herein we described...

Cellular neurothekeoma is a rare cutaneous tumor that occurs more frequently in women. A 68-year-old female with a history of left nasal alar basal cell carcinoma and Guillain-Barré syndrome presented to the clinic with a 3-mm firm skin-colored papule with scattered telangiectasias. Histopathologic examination with immunochemistry of the lesion was consistent with cellular neurothekeoma. It sta...

Neurothekeoma is a rare and benign tumour that occurs most frequently on the head and neck. It is classified as a nerve sheath tumour and epidemiologically occurs in young adults. It is rare to find these tumours occurring in children. The following report describes a case of neurothekeoma in a young girl, its treatment and a review of the literature. Specific histological analysis may reveal a...

Neurothekeoma is an uncommon, benign neoplasm presenting in young adults, primarily on the head and neck. It was initially related to nerve sheath myxoma but with the advent of immunohistochemistry, new insights into its cellular differentiation and origin have emerged, unlinking Neurothekeoma and nerve sheath myxoma. Herein we describe a 19-year-old male who had had a frontal, flesh-colored, a...

Nerve sheath myxomas (NEUROTHEKEOMA) are uncommon tumors of nerve sheet origin. These tumors most frequently arise from in the dermis and subcutaneous tissues of the head and neck, and upper extremities. Neurothekeoma may be either asymptomatic or may present as a painful raised, skin colored, well circumscribed dermal lesion averaging 1 cm in diameter. This entity is especially rare in the foo...