background bone marrow transplantation (bmt)is nowadays used in various hematological disorders including leukemias. hemophilia a & b are sex linked bleeding disorders in which there are various genetic abnormalities in factor viii & ix genes. among various hematological disorders, bleeding disorders mainly hemophilia in now widely treated using plasma derived and recombinant factor viii & ix c...

background : the present study aimed to report the characteristics and treatment outcomes of five patients with nasopharyngeal adenoid cystic carcinoma and a literature review. methods : between 2000 and 2009, five consecutive patients (4 men, 1 woman) were diagnosed with nasopharyngeal adenoid cystic carcinoma and treated at our institution. three patients had stage iva (t4n0m0) and two patien...

The purpose of this paper is to develop a systematic literature review on the subject of sustainable supply chain network design during 1990-2016, through a review of 261 papers. In this study, qualitative technique for conducting a systematic literature review was used. To systematize and make the literature review more accurate, content analysis method was used that include data collect...

This project is the first stage of a larger program of research into hazard perception training for motorcyclists. Future stages of the project will investigate what type of environment can be used to teach hazard perception and responding, for example a simulator environment or combination of off-road and simulator training. This document summarises two reports that were prepared as part of th...

McCune-Albright syndrome (MAS) is a rare, heterogenous, clinical condition caused by a rare genetic mutation. The disorder is more common in females and is characterized by a triad of cutaneous, bone and endocrine abnormalities.  We describe a girl patient with MAS having precocious puberty and multiple cafe-au-lait macules and deforming polyostotic fibrous dysplasia of bone. Clinical presentat...

Proliferating pilomatricoma is a distinctive rare variant of pilomatricoma first described in 1997.Very few cases of proliferating pilomatricoma have been reported in the literature until date. This report is a case of 65 years old male presenting with hard nodular lump on the right side of neck slowly increasing in size for the last 8 months. Wide excision of the lump was performed with clear ...

The association of osteomalacia with neurofibromatosis is a very rare entity. Here a 34 year old man, a known case of neurofibromatosis, is reported who presented with bone pain, hypophosphatemia, rena] phosphorus wasting, multiple Looser's pseudofractures, and low bone density. Treatment with high dose calcitriol and phosphate resulted in temporary treatment. Permanent cure was achieved a...

Thyroid tissue located within the upper airway has received only sparse attention in the English literature. Aberrant benign thyroid masses may present as either an unrelated autopsy finding or with symptoms such as dyspnea, hemoptysis or adult -onset asthma. There is no place for medical management in the therapy of these lesions, although the appropriate surgical procedure is not clearly ...

the purpose of this article is to determine elements of strategic thinking in the context of iranian organizations and to find out the interactions and relationships among determined elements. a literature review and also in-depth interviews with experts are conducted to identify strategic thinking elements. interpretive structural modeling methodology is used for analyzing and determining the ...