absractthis study investigated a 63-day boy with end stage renal disease and abdominalcysts. the antenatal sonography detected anhydraminos, posterior urethral valve,and cystic dysplastic kidneys. voiding cystourethrogram revealed two obstructivegiant diverticula which at first looked like enlarged renal pelvis. the patient had persistenturinary tract infection and perforation of diverticula. t...

Cystic dysplasia of the testis is a rare, benign pathologic finding. We present two recent cases of cystic dysplasia of the testis to our practice. The first case involves an 11 month old male presenting with a non-palpable, intra-abdominal left testis. The second case involves a 7 year old male with left scrotal swelling and a history of left renal agenesis. After review of the literature, the...

We report two brothers with a cystic malformation of the kidneys, liver, and pancreas. In both cases the malformation was fatal and the children died shortly after birth. The pathological findings, consisting of multicystic dysplastic kidneys, dilated and dysgenetic bile ducts, dilated pancreatic ducts, and polysplenia, correspond to those reported by Ivemark as renal-hepatic-pancreatic dysplas...

Split hand/split foot malformation is a human developmental disorder characterized by missing central digits and other distal limb malformations. Multicystic renal dysplasia is the most common cause of an abdominal mass in the new born period and is the most common cystic malformation of the kidney in infancy. Here, we report a case of split hand/split foot malformation with a submucosed cleft ...

Single umbilical artery (SUA) is the most common abnormality of the umbilical cord. It is associated with an increased incidence of atresia of hollow organs, renal abnormalities, limb reduction defects and spontaneous abortions. The aetiopathogenesis, although unknown, is attributed to vascular disruption. In this study, 15 foetal autopsies with SUA, seen over a one-year period have been review...

For the first time in 1946 E.L. Potter (1901–1993) described characteristic appearance of stillborns and deceased newborns with bilateral renal agenesis. Due to further observations distinguished syndrome (Q60.6) – a set external signs that are formed due extreme degree oligohydramnios intrauterine compression fetus. Classical is diagnosed by disfunction both kidneys fetus (for example, agenesi...

Although renal abnormalities have been described in children with Alagille's syndrome, cystic kidney disease has not often been documented, and then usually only at necropsy. Three children with Alagille's syndrome are described, in two of whom a unilateral multicystic dysplastic kidney was detected by prenatal ultrasound; in the other, a solitary cortical cyst was found later in childhood. All...

The pathological gross examination of the kidney revealed a cystic mass on the outer surface measuring 6.0 cm in size. Cut surface showed a cavity filled with jelly-like material, clear fluid, and calcified material. Remaining part of the kidney was unremarkable. Microscopic examination of the cystic mass revealed presence of extensive cartilage, sebaceous glands, ciliated columnar epithelial c...

SYNOPSIS The clinical and pathological findings in 150 children submitted to partial or total nephrectomy have been reviewed. Histological examination of the kidney removed at operation showed evidence of renal dysplasia in 76 (51 %). These 76 patients were divided into three main groups on the basis of the pathological changes found in the kidney and the associated urinary tract anomalies. In ...